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Low-grade endometrial stromal sarcoma (LGESS) is a rare malignant tumor affecting younger women presenting as abnormal uterine bleeding in peri menopausal women. Based on the mitotic state, ESS is histologically divided into two groups: high grade (HG) and low grade (LG). LGESS is relatively more common and tends to occur before menopause. LGESS exhibits a more indolent course, but has high relapse potential. For LGESS, hysterectomy is the cornerstone of treatment, however, the role of bilateral salpingo- oophorectomy (BSO), as well as lymphadenectomy including hormonal treatment, chemotherapy and radiotherapy is debated. Here we are reporting a case of low grade stromal sarcoma. By reporting our case, we wish to stress the necessity for a high grade suspicion to diagnose this tumor even in younger women. A prompt diagnosis and timely intervention are keys to improve patient survival.